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Cholestasis
https://pubmed.ncbi.nlm.nih.gov/38034430/ Cholestasis
JPGN Rep. 2023 Oct 9;4(4):e372.
doi: 10.1097/PG9.0000000000000372. eCollection 2023 Nov.
Healthy Patients With AKR1D1 Mutation Not Requiring Primary Bile Acid Therapy: A Case Series
Akihiko Kimura 1 2, Jun Mori 3, Anh-Hoa Nguyen Pham 4, Kim-Oanh Bui Thi 4, Hajime Takei 2, Tsuyoshi Murai 5, Hisamitsu Hayashi 6, Hiroshi Nittono 2
Abstract
https://pubmed.ncbi.nlm.nih.gov/40018910/
J Pediatr Gastroenterol Nutr. 2025 Feb 28.
doi: 10.1002/jpn3.70016. Online ahead of print.
Hepatic venous wedge pressure gradient measurements in intestinal failure associated liver disease
Joseph Valamparampil 1, Rachel M Brown 2, Simon McGuirk 3, Jane Hartley 1, Ye Htun Oo 4, Khalid Sharif 1, Darius Mirza 1 5, Girish L Gupte 1 6
https://pubmed.ncbi.nlm.nih.gov/34900864/ Cholestasis
Front Pediatr. 2021 Nov 24;9:754941.
doi: 10.3389/fped.2021.754941. eCollection 2021.
High Rate of Cytomegalovirus Detection in Cholestatic Preterm Infants
Jonas Teng 1 2, Anne Elwin 1 3, Soley Omarsdottir 4, Giulia Aquilano 3, Mireille Vanpee 5 6, Antal Nemeth 1, Afsar Rahbar 4 7, Kajsa Bohlin 1 3, Björn Fischler 1 6, Cecilia Söderberg-Nauclér 4 7
Abstract
https://pubmed.ncbi.nlm.nih.gov/37976384/ Cholestasis
Hepatology. 2023 Nov 17.
doi: 10.1097/HEP.0000000000000690. Online ahead of print.
LRH-1 agonist DLPC through STAT6 promotes macrophage polarization and prevents parenteral nutrition associated cholestasis in mice
Swati Ghosh 1, Michael W Devereaux 1, Cuining Liu 1, Ronald J Sokol 1 2
Abstract
Background aims: Parenteral nutrition associated cholestasis (PNAC) is important complication in patients with intestinal failure with reduced LRH-1 expression. Here, we hypothesized that LRH-1 activation by its agonist, dilauroylphosphatidylcholine (DLPC), would trigger STAT6 signaling and hepatic macrophage polarization that would mediate hepatic protection in PNAC.
https://pubmed.ncbi.nlm.nih.gov/39440620/ cholestasis
J Pediatr Gastroenterol Nutr. 2024 Oct 23.
doi: 10.1002/jpn3.12392. Online ahead of print.
Natural course and outcomes of children with ubiquitin-specific protease 53 (USP53)-related genetic chronic cholestasis
Seema Alam 1, Bikrant Bihari Lal 1, Aathira Ravindranath 2, Ashish Bavdekar 3, Nirmala Dheivamani 4, Pandey Snehavardhan 5, Aashay Shah 6, Parijat Ram Tripathi 7, Aabha Nagral 8 9, K P Srikanth 10, Ira Shah 11, Somashekara Hosaagrahara Ramakrishna 12, Arya Suchismita 13, Yogesh Waikar 14, Vaibhav Shah 15, Zahabiya Nalwalla 16, Karunesh Kumar 17, Arjun Maria 18, Anupam Sibal 17, Viswanathan M Sivaramakrishnan 19, Nishant Wadhwa 18, A Ashritha 1, Vikrant Sood 1, Rajeev Khanna 1; Indian PFIC Registry
https://pubmed.ncbi.nlm.nih.gov/38006895/ Cholestasis
Review
Lancet Child Adolesc Health. 2023 Nov 22:S2352-4642(23)00259-6.
doi: 10.1016/S2352-4642(23)00259-6. Online ahead of print.
Paediatric research sets new standards for therapy in paediatric and adult cholestasis
Rebecca Jeyaraj 1, Eamonn R Maher 2, Deirdre Kelly 3
Abstract
https://pubmed.ncbi.nlm.nih.gov/37755879/ Cholelithiasis
stroenterol Nutr. 2023 Dec 1;77(6):741-747.
doi: 10.1097/MPG.0000000000003959.Epub 2023 Sep 26.
Pediatric Cholelithiasis in the United States: National Hospitalization Trends, 2006 to 2019
Atu Agawu 1, Christina Kanagawa 2, Janeline Wong 3, Justine Shults 1 4, Chris Feudtner 1, Meenakshi Bewtra 3 4
Abstract
Objectives: Previous studies have shown increasing hospitalizations for pediatric cholelithiasis, but recent trends are unknown. We conducted a national study of pediatric cholelithiasis to characterize recent hospitalization rate trends.
https://pubmed.ncbi.nlm.nih.gov/35087735/ Cholestasis
Pediatr Gastroenterol Hepatol Nutr. 2022 Jan;25(1):70-78.
doi: 10.5223/pghn.2022.25.1.70.Epub 2022 Jan 7.
Predictor of Liver Biochemistry Improvement in Patients with Cytomegalovirus Cholestasis after Ganciclovir Treatment
Gina Puspita 1, Titis Widowati 1, Agung Triono 1
Abstract
http://www.ncbi.nlm.nih.gov/pubmed/26628447
Kremer AE, Gonzales E, Schaap FG, Oude Elferink RP, Jacquemin E, Beuers U. Serum Autotaxin Activity Correlates With Pruritus in Pediatric Cholestatic Disorders. J Pediatr Gastroenterol Nutr. 2016 Apr; 62(4):530-5.
Abstract
OBJECTIVE:
Pruritus is a common symptom of cholestatic liver disorders. The present study aimed at evaluating autotaxin (ATX), a lysophospholipase recently identified as potential cause for cholestatic pruritus, in pediatric cholestatic diseases presenting with or without itching.
METHODS:
https://pubmed.ncbi.nlm.nih.gov/35942658/ Cholestasis
Curr Opin Pediatr. 2022 Aug 4.
doi: 10.1097/MOP.0000000000001156. Online ahead of print.
The cholestatic infant: updates on diagnosis and genetics
Andrew Wehrman 1, Christine K Lee
Affiliations expand
PMID: 35942658
DOI: 10.1097/MOP.0000000000001156
Abstract
Purpose of review: Cholestasis in infants can indicate a serious hepatobiliary disease and requires timely assessment, diagnosis and intervention to prevent progression to serious liver decompensation. This report aims to highlight recently published studies regarding diagnosis and treatment of cholestasis in infants.
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